Unilateral Darier's disease. (Acantholytic dyskeratotic epidermal nevus) Report of a case and review of the subject

Abstract

We present a case of Darier ‘s disease in linear distribution, in a 38 years old woman who consulted for lesions for about 8 years of evolution type hyperqueratosic papules in inferior abdomen in zosteriform distribution, asymptomatic. We present this case although the low frecuency of this entity, because this is a case that its clinical and histopathological presentation are very charaeteristic for this disease and are important to the diagnosis.