Peutz-Jeghers como síndrome cutáneo y poliposis gastrointestinal

Manuel Dávila Rodríguez; Marly Johanna García Sánchez; Verónica Molina Vélez

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Published: 2013-06-15

How to Cite

Dávila Rodríguez, M., García Sánchez, M. J., & Molina Vélez, V. (2013). Case Report: Peutz-Jeghers-like Cutaneous Syndrome and Gastrointestinal Polyposis. Medicina UPB, 32(1), 79-82. https://revistas.upb.edu.co/index.php/medicina/article/view/1625

This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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Societal impact

Manuel Dávila Rodríguez

Northern University , Northern University , Universidad del Norte , Universidad del Norte , Universidad del Norte

Marly Johanna García Sánchez

Pontifical Bolivarian University

Verónica Molina Vélez

Hospital Pablo Tobon Uribe

Abstract

Peutz-Jeghers syndrome (PJS) is a rare disorder of autosomal dominant inheritance, characterized by the association of cutaneous and mucosal pigmentation and intestinal polyps, which are present from childhood and can sometimes lead to intussusception or gastrointestinal bleeding with significant predisposition to malignancy.

Keywords:

syndrome, Peutz-Jeghers syndrome

Author Biographies

Manuel Dávila Rodríguez, Northern University, Northern University, Universidad del Norte, Universidad del Norte, Universidad del Norte

Physician, third-year resident of Internal Medicine, Universidad del Norte. Barranquilla, Colombia

Marly Johanna García Sánchez, Pontifical Bolivarian University

Medical student in internship year, Universidad Pontificia Bolivariana. Medellin Colombia.

Verónica Molina Vélez, Hospital Pablo Tobon Uribe

Dermatologist, teacher, Pablo Tobón Uribe Hospital. Medellin Colombia.

References

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Van Lier M, Mathus-Vliegen E, Wagner A, Van Leerdam M, Kuipers E. High Cumulative Risk of Intussusception in Patients With Peutz Jeghers Syndrome: time to update surveillance guidelines. Am J Gastroenterol. 2010: 1-6.

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